ID 2.4.1.79 DE globotriaosylceramide 3-beta-N-acetylgalactosaminyltransferase. AN beta3GalNAc-T1. AN galactosylgalactosylglucosylceramide beta-D- AN acetylgalactosaminyltransferase. AN globoside synthase. AN globoside synthetase. AN uridine diphosphoacetylgalactosamine-galactosylgalactosylglucosylceramide AN acetylgalactosaminyltransferase. CA a globoside Gb3Cer (d18:1(4E)) + UDP-N-acetyl-alpha-D-galactosamine = CA a globoside Gb4Cer (d18:1(4E)) + H(+) + UDP. CC -!- Globoside is a neutral glycosphingolipid in human erythrocytes and CC has blood-group-P-antigen activity. CC -!- UDP-GalNAc is the only sugar donor that is used efficiently by the CC enzyme: UDP-Gal and UDP-GlcNAc result in very low enzyme activity. CC -!- Lactosylceramide, globoside and gangliosides GM3 and GD3 are not CC substrates. DR O75752, B3GL1_HUMAN; Q920V1, B3GL1_MOUSE; Q793U7, B3GL1_MUSSI; DR Q864U6, B3GL1_PIG ; Q5RAL7, B3GL1_PONAB; Q6AY39, B3GL1_RAT ; //