ID 3.6.3.49 DE Channel-conductance-controlling ATPase. AN Cystic-fibrosis membrane-conductance-regulating protein. CA ATP + H(2)O = ADP + phosphate. CC -!- An animal enzyme that is active in forming a chloride channel, CC the absence of which brings about cystic fibrosis. CC -!- It is also involved in the functioning of other transmembrane CC channels. PR PROSITE; PDOC00185; DR Q07DV2, CFTR_AOTNA ; Q00PJ2, CFTR_ATEAB ; Q09YK5, CFTR_ATEGE ; DR P35071, CFTR_BOVIN ; Q2QLF9, CFTR_CALJA ; Q2QLB4, CFTR_CALMO ; DR Q5U820, CFTR_CANFA ; Q2QLC5, CFTR_CARPS ; Q00552, CFTR_CAVPO ; DR Q2IBA1, CFTR_CHLAE ; Q07DY5, CFTR_COLGU ; Q07E42, CFTR_DASNO ; DR Q2QL74, CFTR_DIDMA ; Q2IBF6, CFTR_GORGO ; Q2QLA3, CFTR_HORSE ; DR P13569, CFTR_HUMAN ; Q108U0, CFTR_LOXAF ; Q7JII8, CFTR_MACFA ; DR Q7JII7, CFTR_MACFU ; Q00553, CFTR_MACMU ; Q9TUQ2, CFTR_MACNE ; DR Q2QL83, CFTR_MICMU ; P26361, CFTR_MOUSE ; Q09YJ4, CFTR_MUNMU ; DR Q07DW5, CFTR_MUNRE ; Q07E16, CFTR_MUSPF ; Q07DX5, CFTR_NOMLE ; DR Q07DZ6, CFTR_ORNAN ; Q2QLH0, CFTR_OTOGA ; Q2QLE5, CFTR_PANTR ; DR Q9TSP5, CFTR_PAPAN ; Q6PQZ2, CFTR_PIG ; Q2IBE4, CFTR_PONAB ; DR Q00554, CFTR_RABIT ; P34158, CFTR_RAT ; Q2IBB3, CFTR_RHIFE ; DR Q09YH0, CFTR_SAIBB ; Q00555, CFTR_SHEEP ; P26362, CFTR_SQUAC ; DR Q5D1Z7, CFTR_TRIVU ; P26363, CFTR_XENLA ; //