ID 4.1.1.94 DE ethylmalonyl-CoA decarboxylase. CA (2S)-ethylmalonyl-CoA + H(+) = butanoyl-CoA + CO2. CC -!- The enzyme, which exists in all vertebrates, decarboxylates CC ethylmalonyl-CoA, a potentially toxic compound that is formed in low CC amounts by the activity of EC 6.4.1.2 and EC 6.4.1.3. CC -!- It prefers the S isomer, and can decarboxylate (R)-ethylmalonyl-CoA CC with lower efficiency. cf. EC 4.1.1.41. CC -!- Formerly EC 4.1.1.n2. DR Q2HJD5, ECHD1_BOVIN; F1NB38, ECHD1_CHICK; F1R6N4, ECHD1_DANRE; DR Q9NTX5, ECHD1_HUMAN; Q9D9V3, ECHD1_MOUSE; Q5R4W0, ECHD1_PONAB; DR Q6AYG5, ECHD1_RAT ; Q5HZQ8, ECHD1_XENLA; Q28C91, ECHD1_XENTR; //