ID 4.2.1.75 DE Uroporphyrinogen-III synthase. AN Hydroxymethylbilane hydro-lyase (cyclizing). AN Uroporphyrinogen-III cosynthase. AN Uroporphyrinogen-III cosynthetase. CA Hydroxymethylbilane = uroporphyrinogen III + H(2)O. CC -!- In the presence of EC 2.5.1.61, forms uroporphyrinogen III from CC porphobilinogen. DR O48721, HEM4_ARATH ; O30120, HEM4_ARCFU ; P21248, HEM4_BACSU ; DR Q59335, HEM4_CHLP8 ; Q8KCJ3, HEM4_CHLTE ; Q59294, HEM4_CLOJO ; DR P09126, HEM4_ECOLI ; P10746, HEM4_HUMAN ; Q58401, HEM4_METJA ; DR O26268, HEM4_METTH ; P51163, HEM4_MOUSE ; Q10QR9, HEM4_ORYSJ ; DR Q59683, HEM4_PROMI ; P48246, HEM4_PSEAE ; Q9L6Q3, HEM4_SALTY ; DR P87214, HEM4_SCHPO ; P42452, HEM4_SYNE7 ; P06174, HEM4_YEAST ; //